TTC8

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Tetratricopeptide repeat domain 8 (TTC8) also known as Bardet–Biedl syndrome 8 is a protein that in humans is encoded by the TTC8 gene.[1]

Function

TTC8 is associated with gamma-tubulin, BBS4, and PCM1 in the centrosome.[1] PCM1 in turn is involved in centriolar replication during ciliogenesis.[2]

TTC8 is located in the cilia of spermatids, retina, and bronchial epithelium cells.[1]

Clinical significance

Mutations in the TTC8 gene is one of 14 genes[3] identified as causal for Bardet–Biedl syndrome.[1][4]

References

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Further reading

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External links

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