Idiopathic interstitial pneumonia
Template:Short description Template:Infobox medical condition (new) Idiopathic interstitial pneumonia (IIP), or noninfectious pneumonia[1] are a class of diffuse lung diseases. These diseases typically affect the pulmonary interstitium, although some also have a component affecting the airways (for instance, cryptogenic organizing pneumonitis). There are seven recognized distinct subtypes of IIP.[2]
Diagnosis
Classification can be complex,[3] and the combined efforts of clinicians, radiologists, and pathologists can help in the generation of a more specific diagnosis.[4][5]
Idiopathic interstitial pneumonia can be subclassified based on histologic appearance into the following patterns:[6][7]
| Histology | Clinical Correlates |
|---|---|
| Desquamative interstitial pneumonia (DIP) | DIP |
| Diffuse alveolar damage (DAD) | ARDS, AIP, TRALI |
| Nonspecific interstitial pneumonia (NSIP) | NSIP |
| Respiratory bronchiolitis | RB-ILD |
| Usual interstitial pneumonia (UIP) | CVD, IPF, drug toxicity, pneumoconiosis |
| Organizing pneumonia | Cryptogenic organizing pneumonia |
| Lymphoid interstitial pneumonia (LIP) | LIP |
Usual interstitial pneumonia is the most common type.[8]
Development
Table 1: Development of the (histologic) idiopathic interstitial pneumonia classification
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Lymphoid interstitial pneumonia was originally included in this category, then excluded, then included again.[9]
References
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- ↑ Leslie KO, Wick MR. Practical Pulmonary Pathology: A Diagnostic Approach. Elsevier Inc. 2005. Template:ISBN.
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External links
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