HPS6

From Wikipedia, the free encyclopedia
Jump to navigation Jump to search

Template:Short description Template:Infobox gene

Hermansky–Pudlak syndrome 6 (HPS6), also known as ruby-eye protein homolog (Ru), is a protein that in humans is encoded by the HPS6 gene.[1]

Function

This intronless gene encodes a protein that may play a role in organelle biogenesis associated with melanosomes, platelet dense granules, and lysosomes.[2] HPS6 along with HPS3 and HPS5 form a stable protein complex named Biogenesis of Lysosome-related Organelles Complex-2 (BLOC-2).[3]

Clinical significance

Mutations in this gene are associated with Hermansky–Pudlak syndrome type 6 characterized by albinism and prolonged bleeding.[1][4]

References

<templatestyles src="Reflist/styles.css" />

  1. a b Script error: No such module "Citation/CS1".
  2. Script error: No such module "citation/CS1".
  3. Script error: No such module "Citation/CS1".
  4. Script error: No such module "Citation/CS1".

Script error: No such module "Check for unknown parameters".

Further reading

<templatestyles src="Refbegin/styles.css" />

  • Script error: No such module "Citation/CS1".
  • Script error: No such module "Citation/CS1".
  • Script error: No such module "Citation/CS1".
  • Script error: No such module "Citation/CS1".
  • Script error: No such module "Citation/CS1".
  • Script error: No such module "Citation/CS1".

External links


Template:Asbox